The present report describes the findings at chest computed tomography angiography of a 28-year-old female patient with heterotaxy syndrome. This syndrome consists of a variety of anomalies of position and morphology of thoracoabdominal organs which do not follow the
situs solitus or
situs inversus arrangement. Imaging studies play a fundamental role in the individualization of the approach to the patient.
Keywords: Heterotaxy syndrome; Situs inversus; Spleen - abnormalities.