OBJECTIVE: To describe the different presentations of craniofacial fibrous dysplasia in a revisional study of 14 computed tomography exams. MATERIALS AND METHODS: The authors have selected 14 cases of craniofacial fibrous dysplasia attended at the Head & Neck Surgery/Otorhinolaryngology Service and Diagnostic Imaging Service of "Hospital Heliópolis", São Paulo, SP, Brazil, between 1991 and 2002. Three of the following most relevant tomographic findings were analyzed: number of bones affected, predominant radiological presentation and the disease uni- or bilaterality. RESULTS: A predominance of a mixed pattern was observed in relation to the disease presentation. Also, contiguous involvement of two or more bones was observed as well as equivalence between cases of unilateral and bilateral craniofacial involvement, possibly due the fact that most patients presented the monostotic type of fibrous dysplasia. CONCLUSION: The knowledge of tomographic features of craniofacial fibrous dysplasia is of paramount importance for surgical planning and post-treatment follow-up.

Keywords: Fibrous dysplasia of bone, Skull, Face, Facial bones, X-ray computed tomography