Fernando Fernandez Hexsel, Letícia Frigo Canazaro, Mariana Capoani, Paula Musa Aguiar, Eiji Suwa, Antonio Carlos Maciel
Radiol Bras 2009;42(4):267-269 - CASE REPORT
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis of unknown etiology, affecting multiple organ system, involving bones, central nervous system, eyes, lungs, mediastinum, kidneys and retroperitoneum. The authors report two cases that progressed with the typical presentation of the disease. Radiological findings were in agreement with literature and guided the diagnosis, confirmed by immunohistochemistry.
PDF Portuguese
Full Text in Portuguese
Full Text in English